Neonatal Systemic Juvenile Xanthogranuloma with an Ominous Presentation and Successful Treatment
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چکیده
منابع مشابه
Neonatal Systemic Juvenile Xanthogranuloma with an Ominous Presentation and Successful Treatment
This case report originated from a case of neonatal multisystemic juvenile xanthogranuloma (JXG). The patient presented with blue muffin rush, cervical mass, bone destruction, lung nodule, hepatosplenomegaly, and coagulopathy and was successfully treated with Langerhans cell histiocytosis (LCH) based chemotherapy treatment. Similar cases in literature were reviewed and it seems that JXG, a rela...
متن کاملJuvenile Xanthogranuloma.
Juvenile xanthogranuloma is a rare disorder which may be present at birth, or appears in infancy. It can also occur in adults of all ages, appears with lesions that may be solitary or multiple nodules several millimeters in diameter. The predilection sites are head and neck, but it may occur on the extremities and trunk also. Internal organs such as lung, kidney, gastrointestinal tract etc. can...
متن کاملSuccessful treatment of necrobiotic xanthogranuloma with intravenous immunoglobulin.
BACKGROUND Necrobiotic xanthogranuloma (NXG) is a rare chronic disorder characterized by firm yellow to red-orange nodules and plaques affecting the face, abdomen, and extremities with the potential for systemic involvement. NXG has a close association with monoclonal gammopathies, and there is a predilection for the development of multiple myeloma. Treatment options are varied due to inconsist...
متن کاملJuvenile xanthogranuloma: dermoscopic pattern.
Palmer and Bowling [1] have recently described the dermoscopic features in 3 cases of juvenile xanthogranuloma (JXG). A dermoscopic pattern characterized by orange-yellow background with ‘clouds’ of paler yellow deposits was observed in all patients. We have had recent occasion to observe many cases of single and multiple JXG and noted a further constant dermoscopic feature, namely branched and...
متن کاملCardiac juvenile xanthogranuloma in an infant presenting with pericardial effusion.
Juvenile xanthogranuloma is a rare histiocytic disorder of childhood mainly affecting skin and rarely deep soft tissues and viscera. We report a 2-month-old infant who presented with respiratory distress secondary to a large pericardial effusion associated with an epicardial mass. Excisional biopsy was performed and the mass was diagnosed as juvenile xanthogranuloma. The child is well without e...
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ژورنال
عنوان ژورنال: Clinical Medicine Insights: Oncology
سال: 2011
ISSN: 1179-5549,1179-5549
DOI: 10.4137/cmo.s6686